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| | Galactosemia |
 | | The best way to ensure that a medication does not contain fillers with galactose is to ask a pharmacist. | | | With continued dietary management, however, many individuals with galactosemia enjoy good health, and are able to lead independent lives. | | | Galactosemia is an inherited disorder characterized by an inability of the body to utilize galactose. |
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http://depts.washington.edu/transmet/gal.html
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| | European Galactosaemia Society (EGS) - Galactosemia in Europe - Endogenous Galactose Production |
| | According to our experience, stable metabolic conditions are reached within 3 h after start of 13C-label infusion. | | | Up to now, in vivo turnover studies have been performed in 20 galactosemic patients. | | | This might - at least in part - be attributable to the production of free galactose from endogenous sources leading to a so-called 'autointoxication' in the patients. |
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http://galactosaemia.com/galactosaemia/endogenous-galactose.html
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| | Glucose galactose malabsorption |
| | The glucose and galactose, if left untransported, draw water out of the body into the intestinal lumen, resulting in diarrhea. | | | Although no cure exists for GGM, patients can control their symptoms (diarrhea) by removing lactose, sucrose, and glucose from their diets. | | | Half of the 200 severe GGM cases found worldwide result from familial intermarriage. |
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http://www.ncbi.nlm.nih.gov/books/bv.fcgi?call=bv.View..ShowSection&rid=gnd.section.228
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| | What is Galactosemia? |
| | The infant, however, later died because of other complications (the baby had been given tea laced with cognac as treatment as well). | | | He and coworkers elucidated the pathway for converting galactose to glucose in the early 50's. | | | Glucose is the sugar used by the body for energy. |
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http://www.galactosemia.org/galactosemia.htm
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| | galactose on Encyclopedia.com |
| | Prevention of nerve edema and increased blood-nerve barrier permeability-surface area product in galactosemic rats by aldose reductase or thromboxane synthetase inhibitors. | | | Effect of galactose and glucose levels and sorbinil treatment on myo-inositol metabolism and Na+-K+ pump activity in cultured neuroblastoma cells. | | | Zopolrestat and High Galactose Effects on Potassium Transport in Human Lens.(Abstract) |
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http://www.encyclopedia.com/html/X/X-galactose.asp
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| | GALT deficiency causes UDP-hexose deficit in human galactosemic cells -- Lai et al. 13 (4): 285 -- Glycobiology |
| | of human galactose metabolism and emphasized the need to develop | | | Greenman, L. and Rathbun, J.C. (1948) Galactose studies in an infant with idiopathic galactose intolerance. | | | Xu, Y.K., Kaufman, F.R., Donnell, G.N., Giudici, T., Alfi, O., and Ng, W.G. (1995) HPLC analysis of uridine diphosphate sugars: decreased concentrations of uridine diphosphate galactose in erythrocytes and cultured skin fibroblasts from classic galactosemia patients. |
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http://glycob.oxfordjournals.org/cgi/content/full/13/4/285
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| | Galactose definition - Medical Dictionary definitions of popular medical terms |
| | Portal Hypertension - Portal hypertension, an increase in blood pressure within the portal venous system. | | | Galactose definition - Medical Dictionary definitions of popular medical terms | | | MedicineNet Home > MedTerms medical dictionary A-Z List > Galactose |
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http://www.medterms.com/script/main/art.asp?articlekey=3534
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| | Galactose - Wikipedia, the free encyclopedia |
| | Two studies have suggested a possible link between galactose in milk and ovarian cancer. | | | It is also synthesized by the body, where it forms part of glycolipids and glycoproteins in several tissues. | | | In the human body, glucose is changed into galactose in order to enable the mammary glands to secrete lactose. |
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http://en.wikipedia.org/wiki/Galactose
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| | Galactose |
| | This is important because such patients are more susceptible to opportunistic pathogens, especially those that target respiratory organs producing such diseases as pneumonia or bronchitis. | | | In addition, Galactose levels were found to be decreased in the intestinal mucins of colon cancer patients, suggesting that the addition of Galactose to the diet could help prevent or reverse the disease. | | | Bowel disorders can affect absorption of galactose, as well as any of the other sugars. |
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http://www.innvista.com/health/nutrition/essensug/galact.htm
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| | GALACTOSEMIA Case Reports Pediatric Oncall |
| | This condition is quite rare and must be considered in a symptomatic patient with normal transferase activity. | | | Treatment:The mainstay of therapy is lactose free diet as failure to eliminate galactose results in progressive liver failure and death. | | | There are several enzymatic variants of galactosemia of which the Duarte Variant has diminished red cell enzyme activity but no clinical significance and some African-American patients have milder symptoms despite the absence of measurable transferase activity in RBCs as these patients retain about 10% enzyme activity in liver and intestinal mucosa. |
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http://www.pediatriconcall.com/fordoctor/casereports/galactosemia.asp
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| | Carbohydrates - Glucose |
| | The treatment for the disorder is to use a formula based upon the sugar sucrose rather than milk with lactose. | | | One baby out of every 18,000 is born with a genetic defect of not being able to utilize galactose. | | | Undiagnosed it may lead to mental retardation, failure to grow, formation of cataracts, and in sever cases death by liver damage. |
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http://www.elmhurst.edu/~chm/vchembook/543galactose.html
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| | MedlinePlus Medical Encyclopedia: Galactosemia |
| | Galactosemia is the inability of the body to use (metabolize) the simple sugar galactose (causing the accumulation of galactose 1-phosphate), which then reaches high levels in the body, causing damage to the liver, central nervous system, and various other body systems. | | | There are 3 forms of the disease: galactose-1 phosphate uridyl transferase deficiency (classic galactosemia, the most common and most severe form), deficiency of galactose kinase, and deficiency of galactose-6-phosphate epimerase. | | | Despite strict avoidance of galactose, mild intellectual impairment may still develop. |
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http://www.nlm.nih.gov/medlineplus/ency/article/000366.htm
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| | Non-Glucose Carbons in Glycolysis |
| | Entry of galactose carbon atoms into the glycolytic pathway. | | | The principal treatment of these disorders is to eliminate lactose from the diet. | | | The third disorder of galactose metabolism result from a deficiency of UDP-galactose-4-epimerase. |
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http://web.indstate.edu/thcme/mwking/non-glucose-sugar-metabolism.html
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| | Total Galactose Application Notes |
| | Serum galactose measurements therefore can be used to diagnose and treat this disease. | | | Simple galactose can also be measured quantitatively with this test. | | | The Astoria-Pacific SPOTCHECK® Analyzer automates the measurement of galactose in the newborn's sample by first hydrolyzing galactose-1-phosphate to simple galactose using alkaline phosphatase. |
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http://www.astoria-pacific.com/aptgal.php3
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| | Glucose Galactose Malabsorption |
| | The glucose and galactose which have not been absorbed through the specialized cells of the small intestine are then poorly absorbed much further along in the intestine. | | | This abnormal absorption may interfere with other intestinal absorption processes. | | | Glucose-Galactose Malabsorption (carbohydrate intolerance) is a genetic disorder characterized by the small intestine's inability to transport and absorb glucose and galactose (sugars which can be broken down no further, or monosaccharides). |
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http://www.peacehealth.org/kbase/nord/nord749.htm
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| | MedlinePlus Medical Encyclopedia: Galactose-1-phosphate uridyltransferase |
| | Continued use of galactose can also result in cataracts, jaundice, liver enlargement, cirrhosis, and mental retardation. | | | As a consequence, galactose accumulates in the blood (galactosemia) and tissues because it cannot be metabolized. | | | About 1 out of 65,000 newborns has a deficiency of the GALT enzyme (deficiencies of the other enzymes are much less common). |
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http://www.nlm.nih.gov/medlineplus/ency/article/003636.htm
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| | Worthington Galactose Oxidase |
| | Specificity: GAO will oxidize galactose and some galactose derivatives in both free and polymeric form. | | | Studies on the Structure and Role of Disulfide Linkages, J Biol Chem 240, 2966, 1965 | | | Hjelm and Tengstrom (1968) reported a comparison of methods using the oxidase and the dehydrogenase for blood galactose concluding that the two were equally good. |
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http://www.worthington-biochem.com/GAO
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| | ARS Publication request: CONTRIBUTION OF PLASMA GALACTOSE AND GLUCOSE TO MILK LACTOSE SYNTHESIS DURING GALACTOSE ... |
| | Despite the galactose ingested, the glucose production in this and our previous fasting studies were essentially the same, i.e. | | | This study combined with previous studies demonstrate that although plasma glucose is the primary source of milk lactose, plasma galactose is a potential substrate for milk lactose during ingestion of galactose. | | | Interpretive Summary: Using an iv infusion of galactose labeled with stable isotopes and oral administration of unlabeled galactose, the present study demonstrated that ingestion of galactose results in direct uptake of galactose by lactating mammary tissue with conversion to both glucose and galactose in lactose. |
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http://ars.usda.gov/research/publications/publications.htm?SEQ_NO_115=150739
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| | Galactose - OneLook Dictionary Search |
| | Phrases that include Galactose: galactose cataract, galactose 1 phosphate, galactose 1 phosphate uridyltransferase, galactose 6 sulfurase, galactose 1-phosphate uridyltransferase, more... | | | galactose : The On-line Medical Dictionary [home, info] | | | galactose : Dorland's Illustrated Medical Dictionary [home, info] |
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http://www.onelook.com/?w=Galactose&ls=a
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| | ChemFinder.Com |
| | alpha-Galactose(D); D-(+)-Galactose; D-Galactose; D(+)GALACTOSE SIGMA GRADE; Gal; Galactose; |
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http://chemfinder.cambridgesoft.com/result.asp?molid=59-23-4
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